From: The liver is a common non-exocrine target in primary Sjögren's syndrome: A retrospective review
| 1 | Lung | Lymphocytic interstitial pneumonia, fibrosing alveolitis, pseudolymphoma, lymphoma, pulmonary amyloidosis |
| 2 | Renal | Renal tubular acidosis type I, nephrogenic diabetes insipidus, chronic interstitial nephritis, immune-mediated glomerulonephritis |
| 3 | Cardiovascular | Myocarditis, pericarditis, pericardial effusion, Raynaud's |
| 4 | Gastrointestinal | Atrophic gastritis, pancreatitis |
| 5 | Vasculitis | Mononeuritis multiplex, axonal neuropathy, purpura |
| 6 | Hematologic | Coombs positive hemolytic anemia, leukopenia, lymphopenia, thrombocytopenia, hypoplasic bone marrow |
| 7 | Peripheral nervous system | Axonal neuropathy, mononeuritis multiplex |
| 8 | Central nervous system | Aseptic meningitis, cerebral vasculitis, CVA, TIAs, multiple sclerosis "like" changes |
| 9 | Endocrine | Autoimmune thyroid disease |
| 10 | Musculoskeletal | Arthritis, arthralgias, myositis |