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Table 1 Non-exocrine clinical features considered part of 1°SS for this study (excluding liver)

From: The liver is a common non-exocrine target in primary Sjögren's syndrome: A retrospective review

1 Lung Lymphocytic interstitial pneumonia, fibrosing alveolitis, pseudolymphoma, lymphoma, pulmonary amyloidosis
2 Renal Renal tubular acidosis type I, nephrogenic diabetes insipidus, chronic interstitial nephritis, immune-mediated glomerulonephritis
3 Cardiovascular Myocarditis, pericarditis, pericardial effusion, Raynaud's
4 Gastrointestinal Atrophic gastritis, pancreatitis
5 Vasculitis Mononeuritis multiplex, axonal neuropathy, purpura
6 Hematologic Coombs positive hemolytic anemia, leukopenia, lymphopenia, thrombocytopenia, hypoplasic bone marrow
7 Peripheral nervous system Axonal neuropathy, mononeuritis multiplex
8 Central nervous system Aseptic meningitis, cerebral vasculitis, CVA, TIAs, multiple sclerosis "like" changes
9 Endocrine Autoimmune thyroid disease
10 Musculoskeletal Arthritis, arthralgias, myositis
  1. CVA: central vascular accident TIA: transient ischemic attack